T-cell lymphoma

Basic details

Preferred term: T-cell lymphoma
Alt. terms: T cell lymphoma | peripheral T-cell lymphoma | PTCL

HPO term: T-cell lymphoma
HPO code: HP:0012190

GenIA ID: 288
Last updated on: 2024-12-12 10:20:02

Cross ref. with other ontologies

NCIT: -
MESH: D016399
EFO: -
OAE: -
SNOMEDCT: -
ICD10: C84.4

Description

A type of lymphoma that originates in T-cells. Note: the term “peripheral” does not refer to the extremities, but identifies PTCL as a cancer that arises in the lymphoid tissues outside of the bone marrow such as lymph nodes, spleen, gastrointestinal tract, and skin.

Hierarchical classification

Reported patients added to GenIA DB

SubjectID Sex Fam.ID Age* Population MatchedTerm Diagnosis Reference & Pub.codes
101023 M 210731 50 German Non-Hodgkin lymphoma PMID:34975878 [Fam.F008:P008]
101076 F 210226 53 German Non-Hodgkin lymphoma PMID:34975878 [Fam.F041:P041]
101088 M 211560 38 German Non-Hodgkin lymphoma PMID:34975878 [Fam.F054:P054]
101133 M 210896 38 Non-Hodgkin lymphoma Immunodeficiency, common variable, 13 PMID:34975878 [Fam.F082:P082]
101160 F 211433 - Non-Hodgkin lymphoma Infantile-Onset Multisystem Autoimmune Disease 1 PMID:34975878 [Fam.F101:P101]
101441 M 212174 19 North American Non-Hodgkin lymphoma Immunodeficiency, common variable, 8 PMID:26206937 [P6]
101808 F 211441 - Non-Hodgkin lymphoma Immunodeficiency, common variable, 2 PMID:34975878 [Fam.F265:P265]
102222 M 214917 44 German Non-Hodgkin lymphoma NFKB1 insufficiency PMID:32278790 [BY.I.1]; PMID:35486341 [P074]; PMID:150198 [Fam.DJ:467]; PMID:36105815 [W295C]
102229 F 214922tree icon - Anaplastic large-cell lymphoma ARPC1B deficiency PMID:32499645 [Fam.ARPC1B:II.1]
103929 M 215279 34 French Non-Hodgkin lymphoma Hyper-IgE recurrent infection syndrome 1 PMID:22751495 [Fam.K10:P12]
103938 M 215285 17 French Non-Hodgkin lymphoma Hyper-IgE recurrent infection syndrome 1 PMID:22751495 [Fam.K16:P20]
103946 F 215290 8 French Non-Hodgkin lymphoma Hyper-IgE recurrent infection syndrome 1 PMID:22751495 [Fam.K20:P25]
103947 F 215291 21 French Non-Hodgkin lymphoma Hyper-IgE recurrent infection syndrome 1 PMID:22751495 [Fam.K21:P26]
104357 M 215496 - French Non-Hodgkin lymphoma Hyper-IgE recurrent infection syndrome 1 PMID:22084479 [P2]
104361 M 215500 - French Non-Hodgkin lymphoma Hyper-IgE recurrent infection syndrome 1 PMID:22084479 [P6]
104365 F 215504 - French Non-Hodgkin lymphoma Hyper-IgE recurrent infection syndrome 1 PMID:22084479 [P10]
104845 F 215579tree icon 35 European Non-Hodgkin lymphoma NFKB1 insufficiency PMID:32278790 [Fam.NZ:II.2(II.2)]; PMID:26279205 [Fam.NZ:II.2(II2)]; PMID:29403474 [Fam.NZ (5):II.2(II2)]; PMID:29806948 [Fam.NZ:II.2(II.2)]; PMID:30323807 [Fam.2:II.2(II.2)]; PMID:150198 [Fam.AC:II.2(109)]
105173 M 215659 - Non-Hodgkin lymphoma PMID:27102614 [Fam.A:I.1(father)]
105280 M 215685tree icon 68 European Non-Hodgkin lymphoma NFKB1 insufficiency PMID:32278790 [Fam.B:I.1(I.1)]; PMID:29477724 [Fam.B:I.1(I:1)]; PMID:150198 [Fam.AV:I.1(242)]
105338 U 215700 63 European T-cell lymphoma NFKB1 insufficiency PMID:32278790 [K.II.1]; PMID:29477724 [Fam.K:II.1(II:1)]; PMID:150198 [Fam.BE:280]
105591 F 215821 16 Caucasian Non-Hodgkin lymphoma Activated p110-delta syndrome 1 PMID:24610295 [Fam.2:II.1(F2P2)]
105910 F 215905 45 Caucasian Non-Hodgkin lymphoma CTLA4 haploinsufficiency with autoimmune infiltration PMID:30250467 [K.II.1]; PMID:29729943 [Fam.K:II.1(K.II.1 (33))]
106042 M 215927 22 North American Non-Hodgkin lymphoma CTLA4 haploinsufficiency with autoimmune infiltration PMID:30250467 [FF.II.1]; PMID:29729943 [Fam.FF:II.1(FF.II.1 (77))]
106164 M 215963 - Turkish Non-Hodgkin lymphoma Immunodeficiency, common variable, 8 PMID:31432443 [P8]
106169 F 215968 - Turkish Non-Hodgkin lymphoma Immunodeficiency, common variable, 8 PMID:31432443 [P13]
107122 U 216341 - gamma-delta-T-cell derived lymphoma NK/T-cell lymphomas 1 PMID:25586472 [G618R]
107123 U 216342 - gamma-delta-T-cell derived lymphoma NK/T-cell lymphomas 1 PMID:25586472 [Y640F]
107134 M 216353 - Anaplastic large-cell lymphoma NK/T-cell lymphomas 1 PMID:23563237 [ALCL-1]
107135 M 216354 - Anaplastic large-cell lymphoma NK/T-cell lymphomas 1 PMID:23563237 [ALCL-2]
107136 M 216355 - T-cell lymphoma NK/T-cell lymphomas 1 PMID:23563237 [PTCL-1]
107137 F 216356 - T-cell lymphoma NK/T-cell lymphomas 1 PMID:23563237 [PTCL-2]

*Age: age reported at the first known time of manifestation; PMID: PubMed ID; GRID: GenIA reference ID (ref. not in PubMed).